Proximal tubular defects (renal Fanconi syndrome) may occur secondary to some inborn errors of metabolism. Shohl’s solution is used in renal Fanconi syndrome for the treatment of metabolic acidosis. Herein, we report a newborn with galactosemia, a solitary kidney and renal Fanconi syndrome who developed hypocalcemic convulsions under Shohl’s solution treatment. Experience and knowledge regarding treatment with Shohl’s solution in neonates is limited. We thus recommend that clinicians should be cautious regarding the possibility of hypocalcemia while administering Shohl’s solution in newborns.
Key words: Hypocalcemia, Shohl’s solution, newborn